An inherited glandular disease affecting the pancreas, the respiratory system, and the apocrine sweat glands. It is usually characterized by chronic obstructive pulmonary disease (the mucous membranes in the glands produce much mucous which block lung passages), pancreatic insufficiency, and abnormally high sweat electrolytes. Sufferers are malnourished because their body does not have the necessary digestive enzymes to absorb nutrients, and loose excessive salt through their sweat glands.

Dietary recommendations have been modified from a low-fat diet to a current high-protein and normal to high-fat dietary content (20% protein, 40% carbohydrate, 40% fat). Non restricted fat diets with adequate enzyme replacement is suggested for children trying to meet their nutritional goals. It is generally a good idea to limit certain foods that cause stimulation of mucus by the mucous membranes and are difficult to digest, such as cooked and processed foods, high-fat dairy products, too many animal products, sugar, and white flour. The diet should consist of lots of raw vegetables, fruits, and raw nuts. Salt supplementation should be taken during periods of thermal stress. For infants with severe pancreatic insufficiency, formulas containing protein hydrolysates and medium chain triglycerides may be used instead of whole milk.

Pancreatin, proteolytic enzymes, multivitamins in double the recommended daily allowance, vitamins B complex, vitamins A and E (preferably taken in the morning with fat-containing meal and pancreatic enzymes for better absorption, vitamin K for proper digestion and vitamin D and primrose oil.

Echinacea, ginger, goldenseal, yarrow tea.